Syndrome of Sturge-Weber-Krabbe: аscientific review and аclinical observation
https://doi.org/10.52485/19986173_2021_1_117
Abstract
The proposed article presented a contemporary literature review of the obscure disease in children - Sturge-Weber syndrome. The review is illustrated by a clinical example of a rare bisymptomatic form of this syndrome manifested by left-sided hemangioma of the skin of the face and neck, the presence of calcifications in the brain matter on the side opposite to the vascular tumor, characteristic convulsive seizures of the "Jacksonian seizures" type, starting also on the side opposite to the cutaneous manifestations.
About the Authors
E. P. Bataeva
Chita State Medical Academy
Russian Federation
Russian Federation
39А Gorky str., Chita, 672000
A. V. Ignatyeva
Chita State Medical Academy
Russian Federation
Russian Federation
39А Gorky str., Chita, 672000
A. N. Kazantseva
Regional children's clinical hospital
Russian Federation
Russian Federation
20 Novobulvarnaya str., Chita, 672000
T. S. Molchanova
Regional children's clinical hospital
Russian Federation
Russian Federation
20 Novobulvarnaya str., Chita, 672000
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Review
For citations:
Bataeva E.P., Ignatyeva A.V., Kazantseva A.N., Molchanova T.S. Syndrome of Sturge-Weber-Krabbe: аscientific review and аclinical observation. Transbaikalian Medical Bulletin. 2021;(1):117-123. (In Russ.) https://doi.org/10.52485/19986173_2021_1_117
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